Chiari 1 malformation with Platybasia

Background. The incidence of CM-I is estimated to be 1/1,000 births. In rare cases, complicated by associations with other malformations the craniocervical junction, including mainly Basilar invagination (BI). Chiari malformation (CM) characterized a congenital posterior cranial fossa cerebellar tonsils herniation through foramen magnum, probably due underdevelopment bony skeleton (exo-occipital and supraoccipital bones). CM may variety malformations, platybasia, basilar occipitalization, although syringomyelia (SM) most commonly observed Case Report. A girl, 14 years old came chief complaint headache, which exacerbated whenever patient coughed or sneezed. also complained about neck pain tingling sensation in her hand. history vomiting seizure has not been found. muscle weakness was On physical examination, GCS score 15 on admission, normal tone reflexes. sensory deficit, level below C4. underwent CT Scan MRI whole spine, 1 platybasia were diagnosed. decompression, postoperatively symptoms deficit gradually improved. Discussion. As an association this syndrome, there as shown flat basioccipt (platybasia) upward odontoid projection. hydrocephalus [3]. Virchow coined term ‘platybasia’ describe abnormal flattening skull base, defect he attributed bone development. addition base skull, displacement (impression) condylar portions occipital bone, caused infolding, impression reduction fossa, consequent protrusion upper cervical spine into anterior brainstem, neurological signs. symptomatology presented CM-1 patients diverse, its severity does correlate degree TH, some asymptomatic cases presenting prominent TH. onset generally develops gradually, however, trauma, coughing/sneezing pregnancy can precipitate event. common treatment for these surgical PCF decompression (alone duraplasty), tonsillectomy, laminectomy, suboccipital cranioplasty are applied. goal procedures decompress magnum increase subarachnoid space order avoid impaction tonsils, reestablish CSF flow reverse Conclusion. This diagnosed suggested literature, done improved clinically